SLC2A1 is discussed above and variants in another transporter gene, SLC25A12 cause AGC1 deficiency which is associated with a severe neurological phenotype with hypomyelination and epilepsy.43 We published the first case of AGC1 deficiency in a patient that started KD at 6 years.6 Our second patient with an early diagnosis of AGC1 deficiency started KD at 5 months. The gene discussed is SLC25A12; the disease is epilepsy.