Approximately 7% of cystic kidney disease cases-sometimes termed atypical cystic kidney disease, are linked to variants in genes, such as GANAB, DNAJB11, HNF1B, PRKCSH, SEC63, ALG8, ALG9, SEC61B, LRP5, and SEC61A1A [34]. This evidence concerns the gene HNF1B and cystic kidney disease.