Blood samples obtained during hypoglycemia revealed findings consistent with HH, including a serum insulin level of 3.2 μIU/mL (reference range (RR): 1.84–12.20 μIU/mL), total ketone bodies of 34 μmol/L (RR: 0–130 μmol/L), acetoacetate at 13 μmol/L (RR: 0–55 μmol/L), 3-OH-butyric acid at 21 μmol/L (RR: 0–85 μmol/L) and non-esterified fatty acids of 219 μEq/L (RR: 140–850 μEq/L), indicating suppressed ketogenesis and lipolysis due to hyperinsulinism. Here, INS is linked to Hypoglycemia.