In the present study, we obtained and characterised in detailthe genetically modified iPSC line ICGi036-A-1, which wasderived from an isogenic line of an FH patient with compoundheterozygosity for pathogenic and likely pathogenic allelicvariants of the LDLR gene, namely c.530C>T (p.Ser177Leu)and c.1054T>C (p.Cys352Arg). This evidence concerns the gene LDLR and familial hyperaldosteronism.