LZTR1 and NF2-related schwannomatosis: In approximately 95% of cases VS occur as a unilateral, sporadic entity but they can also occur as part of the dominantly inherited tumour syndrome NF2-related schwannomatosis (NF2-SWN) where they commonly present as bilateral multifocal tumours afflicting both nerves, or less commonly unilaterally as part of LZTR1-related schwannomatosis [63].