CD4 and pachyonychia congenita: The cases owing to various causes of death varied and included lymphoma recurrence (in the cases of PC-ALCL and MTX-associated primary cutaneous extranodal NK/T-cell lymphoma), lung lymphoma (in the case of primary cutaneous CD8+ aggressive epidermotropic cytotoxic T-cell lymphoma), cardiovascular emboli (in case of SS), upper intestinal hemorrhage (in the cases of ALCL), and progression of underlying disease (in the case of primary cutaneous small/medium CD4+ T-cell lymphoma).