CODE has substantial morbidity and mortality.Patients often require lifelong fluid and nutritional management.3 Genetic causes include pathogenic variants inMYO5B (Microvillus Inclusion Disease (MVID)),4EPCAM (Tufting enteropathy5), NEUROG3 (enteric anendocrinosis6), DGAT1 (protein-losingenteropathy7) andSLC9A3 (congenital sodium diarrhea8). The gene discussed is DGAT1; the disease is microvillus inclusion disease.