DICER1 and pleuropulmonary blastoma: Patients with DICER1 tumor predisposition syndrome are at risk of developing PPB and CBME along with ovarian sex cord-stromal tumors, brain tumors including pineoblastoma and pituitary blastoma, renal sarcoma, Wilms tumor, cystic nephroma, multinodular goiter and carcinoma of the thyroid, nasal chondromesenchymal hamartoma and embryonal rhabdomyosarcoma [9].