The most common mutations associated with MODY involve glucokinase (Gck) (MODY 2), hepatic nuclear factor 1-alpha (Hnf1α) (MODY 3), and hepatic nuclear factor 4-alpha (Hnf4α) (MODY 1), which together account for approximately 94% of MODY cases [67,68,69]. The gene discussed is HNF4A; the disease is MODY.