This is a 33-year-old Chinese male with MEN1, previously diagnosed with insulinoma, who underwent WB-MRI and was found to have a pancreatic lesion, for which he underwent computed tomography (CT) scan of the pancreas and surgery to work up and remove a well-differentiated neuroendocrine tumor, stage III (T1(2)N1M0). The gene discussed is MEN1; the disease is neuroendocrine neoplasm.