The articles primarily reported the aetiology of SNHL as ‘congenital’ and/or ‘early onset’, with some articles focusing on specific target aetiology such as Usher syndrome Type 1, congenital cytomegalovirus (cCMV), connexin 26 mutations, rubella, and autosomal recessive hereditary nonsyndromic deafness. This evidence concerns the gene GJB2 and Usher syndrome.