XRCC4 and dermatofibrosarcoma protuberans: So, four types of tumor have been now reported in patients with XRCC4-related MPD, namely dermatofibrosarcoma, mandibular osteoid osteoma, thalamic glioma, and jejunal gastrointestinal stromal tumor (GIST), respectively at 5, 20, 19 and 30-years-old.