MORC3 and dermatomyositis: Pseudoangioedema has been described in association with antimelanoma differentiation-associated protein 5, anti-SAE, and antitranscriptional intermediary factor 1 antibodies but has not previously been reported in anti-NXP-2 DM.8, 9, 10 Pseudoangioedema of the lips is a rare cutaneous manifestation of DM, and this unusual feature may serve as a clue to promote prompt diagnosis.