A report noted that in 16 patients with PR3‐ANCA‐positive UIP, HRCT patterns reflected UIP in 18.8% of patients, possible UIP in 18.8% of patients, NSIP in 31.3% of patients, and were unclassifiable in 31.3% of patients [20]. Here, PRTN3 is linked to idiopathic pulmonary fibrosis.