Differentiation can be achieved through immunohistochemistry, as neuroendocrine tumors characteristically exhibit diffuse positivity for neuroendocrine markers such as CD56, Synaptophysin, and Chromogranin A. (4) Ectomesenchymal chondromyxoid tumor: This tumor typically occurs on the dorsal side of the tongue and exhibits morphology similar to GLI1-altered mesenchymal tumors characterized by interstitial mucinous change. Here, SYP is linked to neuroendocrine neoplasm.