FTLD-tau is associated with the mutations in the MAPT gene encoding tau protein, and the disease clinically manifests mainly as bvFTD or nvPPA, while FTLD-TDP can be related to the mutations in the progranulin (GRN) or C9orf72 genes, representing the majority of svPPA cases and an important cause of bvFTD [8]. Here, GRN is linked to behavioral variant of frontotemporal dementia.