Patients with PTHrp-producing pNETs seem to have a longer median survival of about 23,5 months [2] compared to other PTHrp-producing solid tumors with a median survival time of 6 weeks [4].For the reported PTHrp-producing pNET who underwent surgery (n = 14), the biochemical cure rate after 2 years was 28 % (4 of 14 patients, Table 2). Here, PTHLH is linked to primitive neuroectodermal tumor.