In addition to the capillary malformation found in SWS, GNAQ and GNA11 mutations have been identified in other vascular malformations or tumors, including congenital hemangioma, tufted angioma, and Kaposiform hemangioendothelioma.[13, 14] Notably, these conditions are not closely associated with the central nervous system (CNS). Here, GNAQ is linked to vascular malformation.