According to the authors, metabolic control was acceptable in all patients during HMF (2–12 months) (Table 6), with no reported metabolic decompensation, except for an initial metabolic crisis shortly after birth before diagnosis for the two infants with CACT or CPT II deficiency (Table S5) [120, 137, 138]. Here, CPT2 is linked to hyperinsulinemic hypoglycemia, familial, 4.