IPA patients were categorized into high (11.90–70.30 ng/mL in plasma and 9.23–71.7 ng/mL in BALF), medium (4.76–11.9 ng/mL in plasma and 2.16–9.23 ng/mL in BALF), and low (0.43–4.76 ng/mL in plasma and 0.09–2.16 ng/mL in BALF) PTX3 groups. Here, PTX3 is linked to Ito hypomelanosis.