As per Fautrel criteria, our patient fulfilled four major [quotidian fever, arthralgias, transient rash (albeit resolving when we saw the patient), PMN >80%] and two minor (maculopapular rash, leukocytosis >10000 per mm3) criteria; while per Yamaguchi criteria, at least five criteria were satisfied [four major (quotidian fever, arthralgias, typical rash, leukocytosis with 80% or more granulocytes) and one minor (negative tests for ANA and RF)] [1,5]. This evidence concerns the gene BTG3 and Increased total leukocyte count.