GLUD1 and inborn organic aciduria: Other metabolopathies, such as glucose transporter type 1 or 2 (GLUT1 and GLUT2) deficiencies, glutamate dehydrogenase 1 (GLUD1) enzyme deficiency, disorders affecting amino acid metabolism such as organic acidemias or other aminoacidopathies, or deficiencies in succinyl-CoA transferase (SCOT) or beta-ketothiolase (BKT) enzymes, responsible for ketolysis defects, also affect glucose homeostasis and increase the risk of hypoglycemia.