KCNJ11 and MODY: Heterozygous mutations in the KCNJ11 gene have been associated with type 2 diabetes mellitus (OMIM: 125853), transient neonatal diabetes mellitus type 3 (OMIM: 610582), permanent neonatal diabetes mellitus type 2 with or without neurological features (OMIM: 618856), and maturity-onset diabetes of the young type 13 (OMIM: 616329), all with autosomal dominant inheritance.