A 35-year Italian study on Evans’ syndrome describes a male preponderance (23/40) with concomitant Evans’ syndrome in 18/40 patients; 9/40 had a family history of autoimmunity, and 24/40 (60%) presented lymphoproliferation and multiple positive autoantibodies (ENA, ANCA, ASMA) .10 Here, ENAH is linked to Evans syndrome.