In order to determine whether this was a conserved feature across other mouse models of SMA, we performed TMT proteomic profiling in the SmnΔ7/Δ7;SMN2 (aka ‘Taiwanese’) and Smn−/−;SmnΔ7/Δ7;SMN2 (aka SMNΔ7) mouse models of SMA at P0, and compared this proteomic profile to the Smn2B/− at P0. Here, SMN2 is linked to proximal spinal muscular atrophy.