Friedreich’s Ataxia (FRDA), caused by an expansion of an abnormal trinucleotide intronic GAA triplet in the FXN gene on chromosome 9 [1], represents the most common cause of hereditary ataxia [2], a large spectrum of conditions that are almost unequivocally related to the presence of a marked and significant involvement of the cerebellar cortex [3]. The gene discussed is FXN; the disease is Friedreich ataxia.