A few novel biomarkers of renal activity associated with AAV-GN have recently been identified, such as plasma colony-stimulating factor 1 receptor (CSF1R), which correlates positively with disease activity, initial serum creatinine, and C1Q levels, but negatively with the glomerular filtration rate (GFR) in adults with AAV-GN [115]. The gene discussed is CSF1R; the disease is ganglioneuroma.