Due to a strong suspicion of ACTH-producing pheochromocytoma, the patient was qualified for right adrenalectomy and prepared with increasing doses of doxazosin and a low dose of bisoprolol, potassium supplementation, parenteral hydration, protein supplementation, and intense insulin titration. The gene discussed is POMC; the disease is hereditary pheochromocytoma-paraganglioma.