TARDBP and inclusion body myopathy with Paget disease of bone and frontotemporal dementia: Next, we examined whether TER94 KD affects the nuclear localization of TBPH, the Drosophila ortholog of mammalian TDP43 (Lukacsovich et al., 1999), because changes in the localization of TDP43 are a well-defined pathological feature of IBMPFD.