VTN and systemic lupus erythematosus: *Additional additive (clinical or immunology) criteria are counted towards the total score as follows: Do not count a criterion if there is a more likely explanation than SLE; occurrence of a criterion on at least one occasion is sufficient; criteria need not occur simultaneously; within each domain (e.g., mucocutaneous, complement proteins), only the highest-weighted criterion is counted toward the total score if more than one is present.