Most mutations in the GJB2 gene cause autosomal recessive deafness 1 (DFNB1), a leading form of NSHL [11], whereas a few mutations in the GJB2 gene have also been reported to cause autosomal dominant deafness 3 (DFNA3) [15, 16]. The gene discussed is GJB2; the disease is nodular sclerosis classical Hodgkin lymphoma.