The SMN protein, which serves an important function in RNA processing, is likely to be involved in the biogenesis of miRNA, as it binds directly to proteins involved in miRNA production and function, including fragile X mental retardation protein (FMRP), KH-type splicing regulatory protein (KSRP), and fused in sarcoma/translocated in liposarcoma (FUS/TLS) [58,59,60]. The gene discussed is KHSRP; the disease is liposarcoma.