BAP1 and chromophobe renal cell carcinoma: The other rare autosomal dominant disorders associated with chRCC include BAP1 tumor predisposition syndrome (BAP1 gene) [19], hereditary paraganglioma/pheochromocytoma (PGL/PCC) syndrome (SDH A/B/C/D genes) [20], Cowden syndrome (PTEN mutations) [21], and tuberous sclerosis (TSC1/2 mutations) [22].