Seven patients were classified as having definite PSP, and two patients were classified as having TAR DNA-binding protein 43 (TDP-43)-positive frontotemporal lobar degeneration (FTLD-TDP): one with FTLD/MND-TDP and one with FTLD-TDP related to a TANK-binding kinase 1 (TBK1) mutation (Supplemental Table 1). The gene discussed is TBK1; the disease is frontotemporal dementia.