The antibody profile of myositis-associated antibody, ANA, and anti-ENA antibody of the 10 patients who had IIM with or without ILD in the cohort is summarized in Table 2; 7 of the 10 patients were strongly positive for anti-SAE1 autoantibody, whereas the remaining 3 patients were weakly positive for anti-SAE1 autoantibody. Here, SAE1 is linked to acquired idiopathic inflammatory myopathy.