Polymorphisms and haplotypes of MUC5B and TOLLIP have been suggested as prognosticators of functional or radiographic status, or both, in fHP, highlighting the presence of commonalities in terms of host defense and immune response between IPF and fHP.76, 77, 78 Genetic analysis of patients with fibrotic ILDs including fHP showed that telomere-related lung fibrosis was heterogeneous diagnostically, but uniformly progressive.35 Here, MUC5B is linked to idiopathic pulmonary fibrosis.