The pathological finding of poorly formed endothelial cells is the primary criterion for identifying EHE, but It is also proved that immunohistochemistry for CAMTA1 expression of nuclear is a significant method to distinguish EHE from other epithelioid vascular tumors including epithelioid angiosarcoma, epithelioid sarcoma which have the mimic histologic features with the expression of TFE3 by immunohistochemistry being another candidate method (30, 31). This evidence concerns the gene CAMTA1 and epithelioid sarcoma.