TFE3 and alveolar soft part sarcoma: Primary pulmonary ASPS affects the lungs specifically and accounts for <1% of all lung tumors.[11,12] A literature review of primary pulmonary ASPS was conducted, only 6 cases had been reported so far,[5–7,9,10,13] and only 2 of which had confirmed the presence of ASPSCR1–TFE3 fusion.[6,7] To the best of our knowledge, this was the third case of primary pulmonary ASPS with confirmed ASPSCR1–TFE3 fusion, and the clinical characteristics of the 3 cases were presented in Table 1.