The postmortem analysis of the newborn patient with the novel MMUT genotype revealed liver steatosis and damage to the brain and midbrain, consistent with previous reports [1,7], as well as bone marrow hypocellularity [37], and hyperplasia with increased number of pancreatic islets of Langerhans (Figs. 4 A-B), suggestive of noninsulinoma pancreatogenous hypoglycemia syndrome (NIPHS), formerly known as nesidioblastosis. The gene discussed is MMUT; the disease is familial hyperinsulinism.