ARMC5 and Cowden syndrome 1: However, as abdominal CT scans become more common, an increasing number of cases are being diagnosed with PBMAH.[8] The mortality and morbidity of PBMAH depend mainly on the treatment received and the complications of CS, such as arterial hypertension and infections.[9] Sporadic PBMAH mainly affects women,[10] while in patients with ARMC5 mutations, it affects both genders equally.[11] It is usually diagnosed in patients aged 40 to 60 years, often after several years or decades of disease progression.