The primary diagnosis for LT was IPF (n = 24), scleroderma (n = 6), emphysema (n = 4), CF (n = 3), sarcoidosis (n = 3), pulmonary GVHD (n = 3), COPD (n = 2), pulmonary veno-occlusive disease (n = 1), pulmonary hypertension (n = 1), lymphangioleiomyomatosis (n = 1), combined pulmonary fibrosis and emphysema (n = 1), and alpha-1 antitrypsin-related COPD (n = 1). This evidence concerns the gene SERPINA1 and scleroderma.