ABCB11 and Wilson disease: The authors identified a homozygous variant in the ATP-binding cassette, sub-family B member 11 gene as a precipitator of bile accumulation, responsible for inflammation and destruction of biliary ducts resulting in BA, particularly in the Vietnamese population.11 The case presented here is unique, involving a Polynesian male with coexisting BA and WD, a scenario not reported in the literature (Figure 1).