Based on the proband’s age at diagnosis (adolescence), a strong family history of diabetes in both parents and maternal grandfather, short stature, presence of renal cyst and uterine malformation (a Faguer (7) [or HNF1B] score of 12), and absence of GAD antibodies, the diagnosis of HNF1B MODY was suspected. This evidence concerns the gene HNF1B and Renal cyst.