In conclusion, LMNA mutations may be a rare cause of DCM and the initial presenting symptom may be aberrancy in the conduction system resulting in arrythmias, therefore, a comprehensive screening with the inclusion of a comprehensive history and physical, laboratory, and cardiovascular assessment should be conducted to rule out other causes of arrythmias and aid in the diagnosis of a genetic cause. Here, LMNA is linked to familial dilated cardiomyopathy.