The so-called Mitchell–Riley syndrome (OMIM #615710), another rare syndromic form of NDM, is a condition caused by homozygous mutation in the RFX6 gene and is characterized by pancreatic hypoplasia leading to permanent NDM, duodenal and jejunal atresia, and gall bladder agenesis [34]. Here, RFX6 is linked to neonatal diabetes mellitus.