MAX and hereditary pheochromocytoma-paraganglioma: In half of the cases, an association with a genetic variant has been reported, mainly in genes involved in predisposition to pheochromocytoma and paraganglioma such as SDHA (OMIM 614165), SDHB (OMIM 115310), SDHC (OMIM 605373) and SDHD (OMIM 168000) genes coding for the subunits of succinate dehydrogenase, and MAX (OMIM 171300) (46, 55–59).