Among the children displaying hypertension within the first year of life (n = 12), the majority was diagnosed with ARPKD (n = 6), followed by biallelic ADPKD, TSC–PKD1 contiguous syndrome (n = 2, respectively), ADPKD (n = 1), and HNF1B-related disorder (n = 1). Here, HNF1B is linked to autosomal recessive polycystic kidney disease.