Among the children displaying hypertension within the first year of life (n = 12), the majority was diagnosed with ARPKD (n = 6), followed by biallelic ADPKD, TSC–PKD1 contiguous syndrome (n = 2, respectively), ADPKD (n = 1), and HNF1B-related disorder (n = 1). The gene discussed is HNF1B; the disease is autosomal dominant polycystic kidney disease.