Among the patients with glomerulopathy, including SRNS and nephritis, monogenic podocytopathies were identified in 49 patients (COQ8B [n = 18], WT1 [n = 9], PAX2 [n = 6], TRPC6 [n = 5], NPHS1 [[n = 2], NPHS2 [n = 2], PLCE1 [n = 1], NUP107 [n = 1], NUP85 [n = 1], NUP93 [n = 1], LMX1B [n = 1], LAMB2 [n = 1], INF2 [n = 1]). This evidence concerns the gene PAX2 and nephritis.