Table 1 provides a summary of the site specific classification of the International Agency for Research on Cancer (IARC) and World Health Organization (WHO) expert consensus proposal. Note that neuroendocrine neoplasms may form part of syndromes, amongst others, multiple endocrine neoplasia type 1 (MEN1—pituitary adenoma, parathyroid hyperplasia and pancreatic tumors) and multiple endocrine neoplasia type 2 (MEN2—parathyroid hyperplasia, medullary thyroid carcinoma and pheochromocytoma) (10). The gene discussed is MEN1; the disease is parathyroid hyperplasia.