Thus far, 14 causative genes linked to MODY have been identified, including ABCC8, APPL1, BLK, CEL, GCK, HNF1A, HNF1B, HNF4A, INS, KCNJ11, KLF11, NEURO1, PAX4, and PDX1 [1]. This evidence concerns the gene HNF1B and MODY.